1.
Blood Adv
; 1(15): 1101-1106, 2017 Jun 27.
Artigo
em Inglês
| MEDLINE
| ID: mdl-29296752
RESUMO
FAS-dependent apoptosis in Vδ1 T cells makes the latter possible culprits for the lymphadenopathy observed in patients with FAS mutations.Rapamycin and methylprednisolone resistance should prompt clinicians to look for Vδ1 T cell proliferation in ALPS-FAS patients.