Segmental Darier's disease: a presentation of difficult diagnosis
An. bras. dermatol
; 90(3,supl.1): 62-65, May-June 2015. ilus
Article
em En
| LILACS
| ID: lil-755778
Biblioteca responsável:
BR1.1
ABSTRACT
Darier's disease is a rare autosomal dominant genodermatosis. It has an estimated prevalence of 1 in 55,000 to 100,000 individuals, regardless of gender. It is characterized by multiple keratotic papules on the seborrheic areas of the trunk, scalp, forehead and flexures, and the clinical picture is worsened by heat, sun exposure, perspiration and mechanical trauma. Histopathology observed loss of epithelial adhesion and abnormal keratinization. About 10% of cases present in the localized form of the disease. We report a case of segmental Darier's Disease Type I and discuss the main characteristics of this condition.
.Palavras-chave
Texto completo:
1
Base de dados:
LILACS
Assunto principal:
Doença de Darier
Idioma:
En
Ano de publicação:
2015
Tipo de documento:
Article