Autosomal dominant familial frontonasal dermoid cysts: a mother and her identical twin daughters.
Int J Pediatr Otorhinolaryngol
; 57(3): 249-53, 2001 Mar.
Article
em En
| MEDLINE
| ID: mdl-11223458
ABSTRACT
A dermoid cyst is an ectodermal cyst that contains an epithelial lining as well as adnexal structures, and may occur in numerous areas of the body. The nasal dermoid accounts for 1% of all dermoid cysts and 3-12% of head and neck dermoid cysts. While there have been familial cases reported, a genetic inheritance for nasal dermoids has not been suggested. We present the first reported case of a mother and her identical twin daughters who were all found to have evidence of frontonasal dermoid cysts. Our case and a review of literature seem to implicate an autosomal dominant inheritance in certain instances of nasal dermoids.
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Base de dados:
MEDLINE
Assunto principal:
Gêmeos
/
Neoplasias Nasais
/
Cisto Dermoide
/
Encefalocele
Idioma:
En
Ano de publicação:
2001
Tipo de documento:
Article