[Erdheim-Chester disease. Apropos of a case with autopsy findings]. / La maladie d'Erdheim-Chester. A propos d'un cas avec étude autopsique.
Ann Pathol
; 21(6): 529-33, 2001 Dec.
Article
em Fr
| MEDLINE
| ID: mdl-11910940
ABSTRACT
Erdheim-Chester's Disease is a very uncommon variety of non-Langerhans histiocytosis of unknown etiology, which characteristically affects long bones bilaterally and symmetrically in adults. It may be accompanied by visceral foci of variable localization and extension determining prognosis. Bone scintigraphy is characteristic enough to evoke the disease but histologic examination of a peripheral specimen is required to confirm the diagnosis spumous histiocytes CD68+, PS100+/-, CD1a-. We describe a case revealed by a severe lung disease with detailed autopsy.
Buscar no Google
Base de dados:
MEDLINE
Assunto principal:
Histiocitose de Células não Langerhans
Idioma:
Fr
Ano de publicação:
2001
Tipo de documento:
Article