[Clinico-physiological characteristics of syncopal conditions in the long QT syndrome (Romano-Ward syndrome)]. / Kliniko-fiziologicheskaia kharakteristika sinkopal'nykh sostoianii pri sindrome udlinennogo intervala Q-T (sindrom Romano-Uorda).

A complex of methods including clinical analysis, ECG, and exercise EEG was used to examine 52 patients aged 2 to 20 years with Romano-Ward syndrome. There were two groups: group I with syncopal attacks, group II without them. The patients with Romano-Ward syndrome had dysfunction of the suprasegmental systems regulated autonomously in the form of functional insufficiency of the mesencephalic activating system. In the patients without syncopal attacks, there was hyperproduction of the theta-rhythm, which may reflect the mechanisms of compensation. According to the EEG readings, criteria for the syndrome gravity and sudden death risk factors were distinguished.