Three-dimensional CT and histopathological findings of airway malacia in Hunter syndrome.
Tokai J Exp Clin Med
; 32(2): 59-61, 2007 Jul 20.
Article
em En
| MEDLINE
| ID: mdl-21319059
ABSTRACT
A 19-year-old man with known Hunter syndrome presented with dyspnea, and was admitted to our hospital. Bronchoscopy revealed tracheal narrowing with excessive granulation tissue formation in the trachea. Three-dimensional CT clearly demonstrated severe stenosis in the trachea and both main bronchi. Autopsy showed granulomatous tissue proliferation and deposition of mucopolysaccharide in the tracheal wall. We demonstrated the clinico-radiological-pathological correlation of bronchial lesions in Hunter syndrome, and emphasized that three-dimensional CT is helpful in deciding upon therapeutic strategy to treat stenosis in the large airway.
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Base de dados:
MEDLINE
Assunto principal:
Estenose Traqueal
/
Tomografia Computadorizada por Raios X
/
Mucopolissacaridose II
/
Imageamento Tridimensional
Idioma:
En
Ano de publicação:
2007
Tipo de documento:
Article