[Erasmus' syndrome with pseudo-tumour masses]. / Un syndrome d'Erasmus avec des masses pseudo-tumorales.
Rev Mal Respir
; 28(7): 924-7, 2011 Sep.
Article
em Fr
| MEDLINE
| ID: mdl-21943540
ABSTRACT
INTRODUCTION:
Erasmus' syndrome involves the association of systemic scleroderma (SS) and exposure to silica. Silicosis may precede the SS but the latter may be the presentation, in which case a history of exposure to silica should be sought as part of the diagnosis. CASE REPORT A 46-year-old man with history of pulmonary tuberculosis presented with dyspnoea and dysphagea. Clinical examination revealed thickening of the facial skin with a pointed nose, erythema and telangiectasia, Raynaud's syndrome and sclerodactyly. A thoracic CT scan revealed bilateral, fibrotic, pseudo-tumoural masses. Antinuclear antibodies, anti-topoisomerase 1 and antihistone were positive.CONCLUSION:
The clinical presentation of Erasmus' syndrome associating systemic scleroderma and pulmonary pseudo-tumours may pose a problem of differential diagnosis from lung cancer. This condition requires regular clinical and radiological monitoring, particularly as both scleroderma and silicosis increase the risk of lung cancer.
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Escleroderma Sistêmico
/
Silicotuberculose
/
Pulmão
Idioma:
Fr
Ano de publicação:
2011
Tipo de documento:
Article