Alveolar soft-part sarcoma of the orbit: report of 2 cases with review of the literature.

ABSTRACT

Alveolar soft-part sarcoma (ASPS) is a translocation-associated sarcoma that occurs most commonly in the lower extremities and rarely in orbit. Only 34 orbital cases have been reported in the literature, and it is often misdiagnosed due to its rare occurrence and nonspecific clinical findings. The optimal treatment remains controversial, although in general, aggressive surgical resection is advocated. Here, the authors present 2 cases of orbital ASPS and a review of the literature.