Ganglioglioma of the spinal cord in neurofibromatosis type 1.
Pediatr Neurosurg
; 49(1): 50-4, 2013.
Article
em En
| MEDLINE
| ID: mdl-24192615
ABSTRACT
The oncologic involvement of the spinal cord in neurofibromatosis type 1 (NF1) is not a typical feature of the disease. Here, we present a case of ganglioglioma of the spinal cord in a child with NF1 and try to define if this tumor can be considered coincidental or not. A 4-year-old boy affected by NF1 was diagnosed with a spinal cord-enhancing tumor extending from C4 to D3, with a disappearance in the T2 MRI sequences of the cerebrospinal fluid signal. The patient underwent a subtotal resection. The pathological exam revealed a ganglioglioma. To the best of our knowledge, only 1 other case of spinal cord ganglioglioma has been described in an NF1 patient. We suggest considering ganglioglioma in the differential diagnosis of an NF1 patient with a spinal cord tumor due to its favorable survival rate, especially in relation to the anatomical and surgical issues of this tumor that do not always entail a gross total resection.
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Neoplasias da Medula Espinal
/
Neurofibromatose 1
/
Ganglioglioma
Idioma:
En
Ano de publicação:
2013
Tipo de documento:
Article