[Cardiac fibromyxosarcoma with bone metastases : palliative surgical treatment]. / Ossär metastasierendes Fibromyxosarkom des Herzens : Palliative operative Therapie.

ABSTRACT

This article presents the unusual case of a 58-year-old woman with a low-grade cardiac fibromyxosarcoma which was primarily surgically resected and treated with adjuvant chemotherapy. A pulmonary metastasis as well as osteolytic metastatic destruction of the right iliac crest occurred 3 years after primary diagnosis and 2 years later a bone metastasis of the left distal femur was detected. Applying a palliative treatment concept resection of the pulmonary metastasis and an extralesional resection of the bone metastasis of the right iliac crest with plastic reconstruction were performed. Afterwards resection of the left distal femur metastasis and prosthetic reconstruction with distal femur replacement could also be realized. Despite an initial poor prognosis a high quality of life without essential functional limitations could be maintained for more than 6 years in this individual case.