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Mechanism of impaired microtubule-dependent peroxisome trafficking and oxidative stress in SPAST-mutated cells from patients with Hereditary Spastic Paraplegia.
Wali, Gautam; Sutharsan, Ratneswary; Fan, Yongjun; Stewart, Romal; Tello Velasquez, Johana; Sue, Carolyn M; Crane, Denis I; Mackay-Sim, Alan.
Afiliação
  • Wali G; Eskitis Institute for Drug Discovery, Griffith University, Brisbane, Australia.
  • Sutharsan R; Eskitis Institute for Drug Discovery, Griffith University, Brisbane, Australia.
  • Fan Y; Eskitis Institute for Drug Discovery, Griffith University, Brisbane, Australia.
  • Stewart R; The University of Queensland Centre for Clinical Research, Brisbane, Australia.
  • Tello Velasquez J; Eskitis Institute for Drug Discovery, Griffith University, Brisbane, Australia.
  • Sue CM; Kolling Institute of Medical Research, University of Sydney, Sydney, Australia.
  • Crane DI; Eskitis Institute for Drug Discovery, Griffith University, Brisbane, Australia.
  • Mackay-Sim A; Eskitis Institute for Drug Discovery, Griffith University, Brisbane, Australia.
Sci Rep ; 6: 27004, 2016 05 27.
Article em En | MEDLINE | ID: mdl-27229699

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Paraplegia Espástica Hereditária / Neurônios Receptores Olfatórios / Peroxissomos / Células-Tronco Neurais / Espastina / Microtúbulos Idioma: En Ano de publicação: 2016 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Paraplegia Espástica Hereditária / Neurônios Receptores Olfatórios / Peroxissomos / Células-Tronco Neurais / Espastina / Microtúbulos Idioma: En Ano de publicação: 2016 Tipo de documento: Article