Clinical picture and problems of keratoplasty in Richner-Hanhart syndrome (tyrosinemia type II).
Ophthalmologica
; 197(1): 1-6, 1988.
Article
em En
| MEDLINE
| ID: mdl-3054681
ABSTRACT
The Richner-Hanhart syndrome seen in a middle-aged woman is described. The patient had the typical clinical manifestations of tyrosinemia II with a bilateral keratopathy, palmar and plantar hyperkeratosis. The patient was subjected to a specific diet and to perforating keratoplasty. Postoperative systemic therapy with steroids had a negative influence on the clinical manifestations; dendritic lesions which developed on the corneal graft disappeared after interruption of the systemic steroid therapy. This suggests that cortisone treatment after keratoplasty should be avoided in this special metabolic disorder.
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Base de dados:
MEDLINE
Assunto principal:
Tirosina
/
Transplante de Córnea
/
Opacidade da Córnea
/
Erros Inatos do Metabolismo dos Aminoácidos
Idioma:
En
Ano de publicação:
1988
Tipo de documento:
Article