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Taurine alleviates repression of betaine-homocysteine S-methyltransferase and significantly improves the efficacy of long-term betaine treatment in a mouse model of cystathionine ß-synthase-deficient homocystinuria.
Maclean, Kenneth N; Jiang, Hua; Phinney, Whitney N; Keating, Amy K; Hurt, K Joseph; Stabler, Sally P.
Afiliação
  • Maclean KN; Department of Pediatrics, University of Colorado School of Medicine, Aurora, Colorado, USA.
  • Jiang H; Department of Pediatrics, University of Colorado School of Medicine, Aurora, Colorado, USA.
  • Phinney WN; Department of Medicine, University of Colorado School of Medicine, Aurora, Colorado, USA.
  • Keating AK; Department of Pediatrics, University of Colorado School of Medicine, Aurora, Colorado, USA.
  • Hurt KJ; Department of Obstetrics and Gynecology, University of Colorado School of Medicine, Aurora, Colorado, USA.
  • Stabler SP; Department of Medicine, University of Colorado School of Medicine, Aurora, Colorado, USA.
FASEB J ; 33(5): 6339-6353, 2019 05.
Article em En | MEDLINE | ID: mdl-30768359

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Taurina / Betaína / Betaína-Homocisteína S-Metiltransferase / Homocistinúria / Fígado Idioma: En Ano de publicação: 2019 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Taurina / Betaína / Betaína-Homocisteína S-Metiltransferase / Homocistinúria / Fígado Idioma: En Ano de publicação: 2019 Tipo de documento: Article