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R180T variant of δ-ornithine aminotransferase associated with gyrate atrophy: biochemical, computational, X-ray and NMR studies provide insight into its catalytic features.
Montioli, Riccardo; Paiardini, Alessandro; Giardina, Giorgio; Zanzoni, Serena; Cutruzzola, Francesca; Cellini, Barbara; Borri Voltattorni, Carla.
Afiliação
  • Montioli R; Department of Neurosciences, Biomedicine and Movement Sciences, University of Verona, Italy.
  • Paiardini A; Department of Biochemical Sciences "A. Rossi Fanelli", Sapienza University of Rome, Italy.
  • Giardina G; Department of Biochemical Sciences "A. Rossi Fanelli", Sapienza University of Rome, Italy.
  • Zanzoni S; Centro Piattaforme Tecnologiche, University of Verona, Italy.
  • Cutruzzola F; Department of Biochemical Sciences "A. Rossi Fanelli", Sapienza University of Rome, Italy.
  • Cellini B; Department of Experimental Medicine, University of Perugia, Italy.
  • Borri Voltattorni C; Department of Neurosciences, Biomedicine and Movement Sciences, University of Verona, Italy.
FEBS J ; 286(14): 2787-2798, 2019 07.
Article em En | MEDLINE | ID: mdl-30957963

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Ornitina-Oxo-Ácido Transaminase / Atrofia Girata Idioma: En Ano de publicação: 2019 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Ornitina-Oxo-Ácido Transaminase / Atrofia Girata Idioma: En Ano de publicação: 2019 Tipo de documento: Article