Rowell's syndrome: a rare but distinct entity in rheumatology.
BMJ Case Rep
; 13(9)2020 Sep 23.
Article
em En
| MEDLINE
| ID: mdl-32967943
ABSTRACT
Rowell's syndrome is a rare disorder characterised by an association of lupus erythematosus with erythema multiforme (EM)-like skin lesions. EM as the initial clinical presentation of systemic lupus erythematosus is also atypical and even rarer. We report the case of an 18-year-old girl admitted to our hospital with fever and polyarthralgia along with multiple discrete ill-defined target lesions with crust formation over forehead, cheek, external ears, scalp, upper chest and back (predominantly over sun-exposed areas) with ulceration over hard palate. Investigations revealed pancytopaenia, a positive rheumatoid factor, positive antinuclear antibody with a speckled pattern, anti-Smith antibody and strongly positive anti-Ro. Patient was diagnosed with Rowell's syndrome as per clinical and laboratory features. Majority of skin lesions including oral ulcerations subsided gradually after treatment with steroids and hydroxychloroquine.
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Base de dados:
MEDLINE
Assunto principal:
Pancitopenia
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Eritema Multiforme
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Artralgia
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Febre
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Lúpus Eritematoso Sistêmico
Idioma:
En
Ano de publicação:
2020
Tipo de documento:
Article