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The abnormal accumulation of heparan sulfate in patients with mucopolysaccharidosis prevents the elastolytic activity of cathepsin V.
Chazeirat, Thibault; Denamur, Sophie; Bojarski, Krzysztof K; Andrault, Pierre-Marie; Sizaret, Damien; Zhang, Fuming; Saidi, Ahlame; Tardieu, Marine; Linhardt, Robert J; Labarthe, François; Brömme, Dieter; Samsonov, Sergey A; Lalmanach, Gilles; Lecaille, Fabien.
Afiliação
  • Chazeirat T; Université de Tours, Tours, France; INSERM, UMR 1100, Centre d'Etude des Pathologies Respiratoires (CEPR), Team "Mécanismes Protéolytiques Dans l'Inflammation", Tours, France. Electronic address: thibault.chazeirat@etu.univ-tours.fr.
  • Denamur S; Université de Tours, Tours, France; INSERM, UMR 1100, Centre d'Etude des Pathologies Respiratoires (CEPR), Team "Mécanismes Protéolytiques Dans l'Inflammation", Tours, France; Pediatric Department, Reference Center for Inborn Errors of Metabolism ToTeM, CHRU Tours, France. Electronic address: sophie
  • Bojarski KK; Faculty of Chemistry, University of Gdansk, Poland. Electronic address: krzysztof.bojarski@ug.edu.pl.
  • Andrault PM; Department of Oral Biological and Medical Sciences, University of British Columbia, Vancouver, British Columbia, Canada. Electronic address: andrault_pm@yahoo.fr.
  • Sizaret D; Anatomical Pathology and Cytology Department, Bretonneau Hospital, CHRU Tours, France. Electronic address: D.SIZARET@chu-tours.fr.
  • Zhang F; Center for Biotechnology and Interdisciplinary Studies, Rensselaer Polytechnic Institute, Troy, New York, USA. Electronic address: zhangf2@rpi.edu.
  • Saidi A; Université de Tours, Tours, France; INSERM, UMR 1100, Centre d'Etude des Pathologies Respiratoires (CEPR), Team "Mécanismes Protéolytiques Dans l'Inflammation", Tours, France. Electronic address: ahlame.saidi@univ-tours.fr.
  • Tardieu M; Pediatric Department, Reference Center for Inborn Errors of Metabolism ToTeM, CHRU Tours, France. Electronic address: M.TARDIEU@chu-tours.fr.
  • Linhardt RJ; Center for Biotechnology and Interdisciplinary Studies, Rensselaer Polytechnic Institute, Troy, New York, USA. Electronic address: linhar@rpi.edu.
  • Labarthe F; Pediatric Department, Reference Center for Inborn Errors of Metabolism ToTeM, CHRU Tours, France; INSERM, UMR 1069, Nutrition, Croissance et Cancer (N2C), Tours, France. Electronic address: francois.labarthe@univ-tours.fr.
  • Brömme D; Department of Oral Biological and Medical Sciences, University of British Columbia, Vancouver, British Columbia, Canada. Electronic address: dbromme@dentistry.ubc.ca.
  • Samsonov SA; Faculty of Chemistry, University of Gdansk, Poland. Electronic address: sergey.samsonov@ug.edu.pl.
  • Lalmanach G; Université de Tours, Tours, France; INSERM, UMR 1100, Centre d'Etude des Pathologies Respiratoires (CEPR), Team "Mécanismes Protéolytiques Dans l'Inflammation", Tours, France. Electronic address: gilles.lalmanach@univ-tours.fr.
  • Lecaille F; Université de Tours, Tours, France; INSERM, UMR 1100, Centre d'Etude des Pathologies Respiratoires (CEPR), Team "Mécanismes Protéolytiques Dans l'Inflammation", Tours, France. Electronic address: fabien.lecaille@univ-tours.fr.
Carbohydr Polym ; 253: 117261, 2021 Feb 01.
Article em En | MEDLINE | ID: mdl-33278943

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Índice de Gravidade de Doença / Brônquios / Cisteína Endopeptidases / Catepsinas / Mucopolissacaridoses / Células Epiteliais / Heparitina Sulfato Idioma: En Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Índice de Gravidade de Doença / Brônquios / Cisteína Endopeptidases / Catepsinas / Mucopolissacaridoses / Células Epiteliais / Heparitina Sulfato Idioma: En Ano de publicação: 2021 Tipo de documento: Article