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Challenges in the management of acute intermittent porphyria with recurrent attacks during pregnancy: A case report.
Vassiliou, Daphne; Lempessi, Chariklia; Harper, Pauline; Sardh, Eliane.
Afiliação
  • Vassiliou D; Department of Endocrinology and Nephrology, Inflammation and Infection Karolinska University Hospital Stockholm Sweden.
  • Lempessi C; Centre for Inherited Metabolic Diseases (CMMS) Porphyria Centre Sweden Karolinska University Hospital Stockholm Sweden.
  • Harper P; Department of Molecular Medicine and Surgery Karolinska Institutet Stockholm Sweden.
  • Sardh E; Department of Medicine Örebro University Hospital Örebro Sweden.
Clin Case Rep ; 8(12): 2483-2487, 2020 Dec.
Article em En | MEDLINE | ID: mdl-33363763
ABSTRACT
In cases of recurrent attacks of acute porphyria during pregnancy, prophylactic administration of heme arginate should be considered. Clinical and biochemical monitoring of the disease and a close collaboration with a porphyria center are crucial.
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Texto completo: 1 Base de dados: MEDLINE Idioma: En Ano de publicação: 2020 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Idioma: En Ano de publicação: 2020 Tipo de documento: Article