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Muscle metabolic remodelling patterns in Duchenne muscular dystrophy revealed by ultra-high-resolution mass spectrometry imaging.
Dabaj, Ivana; Ferey, Justine; Marguet, Florent; Gilard, Vianney; Basset, Carole; Bahri, Youssef; Brehin, Anne-Claire; Vanhulle, Catherine; Leturcq, France; Marret, Stéphane; Laquerrière, Annie; Schmitz-Afonso, Isabelle; Afonso, Carlos; Bekri, Soumeya; Tebani, Abdellah.
Afiliação
  • Dabaj I; Department of Neonatal Pediatrics, Intensive Care and Neuropediatrics, Rouen University Hospital, 76031, Rouen, France.
  • Ferey J; Normandie Univ, UNIROUEN, CHU Rouen, INSERM U1245, 76000, Rouen, France.
  • Marguet F; Department of Metabolic Biochemistry, Rouen University Hospital, 76031, Rouen, Cedex, France.
  • Gilard V; Normandie Univ, UNIROUEN, CHU Rouen, INSERM U1245, 76000, Rouen, France.
  • Basset C; Department of Pathology, Rouen University Hospital, Rouen, France.
  • Bahri Y; Department of Metabolic Biochemistry, Rouen University Hospital, 76031, Rouen, Cedex, France.
  • Brehin AC; Department of Neurosurgery, Rouen University Hospital, Rouen, France.
  • Vanhulle C; Department of Pathology, Rouen University Hospital, Rouen, France.
  • Leturcq F; Normandie Univ, COBRA UMR 6014 Et FR 3038 Univ Rouen; INSA Rouen; CNRS IRCOF, 1 Rue TesnieÌre, 76821, Mont-Saint-Aignan Cedex, France.
  • Marret S; Department of Genetics and Reference Center for Developmental Disorders, Normandy Center for Genomic and Personalized Medicine, Normandie Univ, UNIROUEN, Inserm U1245 and Rouen University Hospital, 76000, Rouen, France.
  • Laquerrière A; Department of Neonatal Pediatrics, Intensive Care and Neuropediatrics, Rouen University Hospital, 76031, Rouen, France.
  • Schmitz-Afonso I; APHP, Laboratoire de Génétique Et Biologie Moléculaire, HUPC Cochin, Paris, France.
  • Afonso C; Department of Neonatal Pediatrics, Intensive Care and Neuropediatrics, Rouen University Hospital, 76031, Rouen, France.
  • Bekri S; Normandie Univ, UNIROUEN, CHU Rouen, INSERM U1245, 76000, Rouen, France.
  • Tebani A; Normandie Univ, UNIROUEN, CHU Rouen, INSERM U1245, 76000, Rouen, France.
Sci Rep ; 11(1): 1906, 2021 01 21.
Article em En | MEDLINE | ID: mdl-33479270

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Músculo Esquelético / Distrofia Muscular de Duchenne / Metabolômica Idioma: En Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Músculo Esquelético / Distrofia Muscular de Duchenne / Metabolômica Idioma: En Ano de publicação: 2021 Tipo de documento: Article