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Atlantoaxial instability in a case of Maroteaux-Lamy syndrome.
Shah, Abhidha; Jadhav, Neha; Dandpat, Saswat; Goel, Atul.
Afiliação
  • Shah A; Department of Neurosurgery, K.E.M. Hospital and Seth G.S. Medical College, Mumbai, Maharashtra, India.
  • Jadhav N; Department of Neurosurgery, K.E.M. Hospital and Seth G.S. Medical College, Mumbai, Maharashtra, India.
  • Dandpat S; Department of Neurosurgery, K.E.M. Hospital and Seth G.S. Medical College, Mumbai, Maharashtra, India.
  • Goel A; Department of Neurosurgery, K.E.M. Hospital and Seth G.S. Medical College, Mumbai, Maharashtra, India.
J Craniovertebr Junction Spine ; 12(1): 91-94, 2021.
Article em En | MEDLINE | ID: mdl-33850389
ABSTRACT
A relatively rare report of an 8-year-old girl with Maroteaux-Lamy syndrome that is Type VI mucopolysaccharidosis who presented with symptoms of spastic quadriparesis related to atlantoaxial instability is presented. Atlantoaxial stabilization resulted in rapid and sustained neurological recovery.
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Texto completo: 1 Base de dados: MEDLINE Idioma: En Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Idioma: En Ano de publicação: 2021 Tipo de documento: Article