Megalencephaly-capillary malformation syndrome and associated hydrocephalus: treatment options and revision of the literature.
Childs Nerv Syst
; 37(8): 2441-2449, 2021 08.
Article
em En
| MEDLINE
| ID: mdl-34047857
ABSTRACT
PURPOSE:
We describe our series of 4 patients with megalencephaly-capillary malformation syndrome (MCAP) and review the literature in order to assess the optimal treatment for the associated hydrocephalus.METHODS:
We review our institutional series of hydrocephalus associated with MCAP and review the literature, analyzing the causes that could originate the hydrocephalus and the different types of treatments proposed for them.RESULTS:
Of our patients treated with ventriculoperitoneal (VP) shunt, one suffered a surgical revision of the shunt and died due to a cranial trauma unrelated to her syndrome or the previous shunt surgery, and the other did not undergo surgical revisions until the end of her follow-up. Our patients treated with endoscopic third ventriculostomy (ETV) have improved their symptomatology and have not suffered of any complications related to the hydrocephalus after the ETV surgery.CONCLUSIONS:
We update the treatment of MCAP-associated hydrocephalus and propose ETV as a valid treatment, as it seems a safe procedure with a low rate of complications.Palavras-chave
Texto completo:
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Base de dados:
MEDLINE
Assunto principal:
Terceiro Ventrículo
/
Neuroendoscopia
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Megalencefalia
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Hidrocefalia
Idioma:
En
Ano de publicação:
2021
Tipo de documento:
Article