Late onset parkinsonian syndrome in Hallervorden-Spatz disease.
J Neurol Neurosurg Psychiatry
; 50(12): 1665-8, 1987 Dec.
Article
em En
| MEDLINE
| ID: mdl-3437298
ABSTRACT
Two siblings, from consanguineous parents, developed in their twenties a Parkinsonian syndrome. In the elder, the disease evolved for 13 years and the necropsic study was diagnostic of Hallervorden-Spatz disease. The younger sibling is severely affected after 12 years of the disorder. Several CT and one MR studies done in this patient during the last 4 years have been normal. Ultrastructural studies of the bone marrow histiocytes and blood lymphocytes disclosed peculiar inclusions. Bromocriptine in low doses proved to be a beneficial therapy for this patient.
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Doença de Parkinson Secundária
/
Doenças dos Gânglios da Base
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Encéfalo
/
Neurodegeneração Associada a Pantotenato-Quinase
Idioma:
En
Ano de publicação:
1987
Tipo de documento:
Article