Discordant Atrioventricular Connections in Situs Inversus, Dextrocardia with Double Outlet Right Ventricle, Pulmonary Stenosis, and Anomalous Coronary Artery: A Rare Case Report.
World J Pediatr Congenit Heart Surg
; 13(2): 257-259, 2022 03.
Article
em En
| MEDLINE
| ID: mdl-34661458
ABSTRACT
We report a case of a 2-year-old female presenting with cyanosis since birth and having rare cardiac anatomy of visceral situs inversus, dextrocardia, discordant atrioventricular connections with double outlet right ventricle, atrial communication, subaortic interventricular communication, anteriorly leftward aorta with right aortic arch, single coronary artery with a branch crossing right ventricle outflow tract, pulmonary stenosis, and bilateral superior vena cava. Corrective repair with atrial switch (Senning technique), intracardiac baffle, and right ventricle outflow reconstruction was successfully performed with challenges from altered anatomical location and orientation of the heart and abnormal coronary artery.
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Base de dados:
MEDLINE
Assunto principal:
Estenose da Valva Pulmonar
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Situs Inversus
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Dupla Via de Saída do Ventrículo Direito
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Dextrocardia
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Síndrome de Heterotaxia
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Comunicação Interventricular
Idioma:
En
Ano de publicação:
2022
Tipo de documento:
Article