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MG132 Induces Progerin Clearance and Improves Disease Phenotypes in HGPS-like Patients' Cells.
Harhouri, Karim; Cau, Pierre; Casey, Frank; Guedenon, Koffi Mawuse; Doubaj, Yassamine; Van Maldergem, Lionel; Mejia-Baltodano, Gerardo; Bartoli, Catherine; De Sandre-Giovannoli, Annachiara; Lévy, Nicolas.
Afiliação
  • Harhouri K; Marseille Medical Genetics (MMG), INSERM U 1251, Aix Marseille Université, 13005 Marseille, France.
  • Cau P; Progelife, 13002 Marseille, France.
  • Casey F; Progelife, 13002 Marseille, France.
  • Guedenon KM; Royal Belfast, Pediatric Cardiology, Hospital for Sick Children, Belfast BT9 7AB, Northern Ireland, UK.
  • Doubaj Y; CHU Sylvanus Olympio de Lomé, Unité de Génétique Humaine, Lomé BP 1515, Togo.
  • Van Maldergem L; Département de Génétique Médicale, Institut National d'Hygiène, Rabat 11400, Morocco.
  • Mejia-Baltodano G; Centre de Génétique Humaine, CHU Université de Franche-Comté, 25000 Besancon, France.
  • Bartoli C; Departamento de Genética, Ministerio de Salud de Nicaragua, Hospital Infantil "Manuel de Jesús Rivera", Managua 12079, Nicaragua.
  • De Sandre-Giovannoli A; Marseille Medical Genetics (MMG), INSERM U 1251, Aix Marseille Université, 13005 Marseille, France.
  • Lévy N; Marseille Medical Genetics (MMG), INSERM U 1251, Aix Marseille Université, 13005 Marseille, France.
Cells ; 11(4)2022 02 10.
Article em En | MEDLINE | ID: mdl-35203262

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Progéria Idioma: En Ano de publicação: 2022 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Progéria Idioma: En Ano de publicação: 2022 Tipo de documento: Article