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Expert management of congenital portosystemic shunts and their complications.
McLin, Valérie Anne; Franchi-Abella, Stéphanie; Brütsch, Timothée; Bahadori, Atessa; Casotti, Valeria; de Ville de Goyet, Jean; Dumery, Grégoire; Gonzales, Emmanuel; Guérin, Florent; Hascoet, Sebastien; Heaton, Nigel; Kuhlmann, Béatrice; Lador, Frédéric; Lambert, Virginie; Marra, Paolo; Plessier, Aurélie; Quaglia, Alberto; Rougemont, Anne-Laure; Savale, Laurent; Sarma, Moinak Sen; Sitbon, Olivier; Superina, Riccardo Antonio; Uchida, Hajime; van Albada, Mirjam; van der Doef, Hubert Petrus Johannes; Vilgrain, Valérie; Wacker, Julie; Zwaveling, Nitash; Debray, Dominique; Wildhaber, Barbara Elisabeth.
Afiliação
  • McLin VA; Swiss Pediatric Liver Center, Gastroenterology, Hepatology and Pediatric Nutrition Unit, Department of Pediatrics, Gynecology and Obstetrics, University of Geneva, Geneva, Switzerland.
  • Franchi-Abella S; ERN RARE LIVER.
  • Brütsch T; Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.
  • Bahadori A; AP-HP, Centre de référence des maladies rares du foie de l'enfant, Service de radiologie pédiatrique diagnostique et interventionnelle, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.
  • Casotti V; BIOMAPS UMR 9011 CNRS, INSERM, CEA, Orsay, France.
  • de Ville de Goyet J; ERN RARE LIVER.
  • Dumery G; ERN Transplant Child.
  • Gonzales E; Communication in Science, rue du Tunnel 7, Carouge, Switzerland.
  • Guérin F; Department of Pediatrics, Gynecology and Obstetrics, University of Geneva, Geneva, Switzerland.
  • Hascoet S; Pediatric Hepatology, Gastroenterology and Transplant Centre, ASST Papa Giovanni XXIII Hospital, Bergamo, Italy.
  • Heaton N; ERN Transplant Child.
  • Kuhlmann B; Pediatric Department for the Treatment and Study of Abdominal Diseases and Abdominal Transplantation, ISMETT UPMC, Palermo, Italy.
  • Lador F; Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.
  • Lambert V; AP-HP, Service de gynécologie et d'obstétrique, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.
  • Marra P; Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.
  • Plessier A; AP-HP, Centre de référence des maladies rares du foie de l'enfant, FHU Hepatinov, Service d'hépatologie et transplantation hépatique pédiatriques, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.
  • Quaglia A; INSERM UMRS_1193, Orsay, France.
  • Rougemont AL; ERN RARE LIVER.
  • Savale L; ERN Transplant Child.
  • Sarma MS; Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.
  • Sitbon O; AP-HP, Service de chirurgie pédiatrique, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.
  • Superina RA; ERN RARE LIVER.
  • Uchida H; ERN Transplant Child.
  • van Albada M; Department of Congenital Heart Diseases, Hôpital Marie Lannelongue, France.
  • van der Doef HPJ; INSERM UMR_S 999, Université Paris, France.
  • Vilgrain V; Institute of Liver Studies, Kings College Hospital, London, England.
  • Wacker J; Pediatric Endocrinology, Cantonal Hospital Aarau KSA, Aarau, Switzerland.
  • Zwaveling N; Service de Pneumologie, University of Geneva, Geneva, Switzerland.
  • Debray D; Cardiologie congénitale, Institut Mutualiste Montsouris, Paris, France.
  • Wildhaber BE; AP-HP, Centre de référence des maladies rares du foie de l'enfant, Service de radiologie pédiatrique diagnostique et interventionnelle, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.
JHEP Rep ; 6(1): 100933, 2024 Jan.
Article em En | MEDLINE | ID: mdl-38234409
ABSTRACT
Congenital portosystemic shunts are often associated with systemic complications, the most challenging of which are liver nodules, pulmonary hypertension, endocrine abnormalities, and neurocognitive dysfunction. In the present paper, we offer expert clinical guidance on the management of liver nodules, pulmonary hypertension, and endocrine abnormalities, and we make recommendations regarding shunt closure and follow-up.
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Texto completo: 1 Base de dados: MEDLINE Idioma: En Ano de publicação: 2024 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Idioma: En Ano de publicação: 2024 Tipo de documento: Article