Gorlin-Goltz Syndrome - A Rare Case Entity in Young Child.
Prague Med Rep
; 125(1): 69-78, 2024.
Article
em En
| MEDLINE
| ID: mdl-38470440
ABSTRACT
Gorlin-Goltz syndrome (GGS) is an infrequent multisystemic disease with an autosomal dominant trait, which depicted presence of numerous basal cell carcinoma in conjunction with multiorgan abnormalities. This syndrome may be diagnosed early by a dentist by routine radiographic exams in the first decade of life, since the keratocystic odontogenic tumour are usually one of the first manifestations of the syndrome. This article includes a case report of the GGS with regard to its history, incidence, etiology, features, investigations, diagnostic criteria, keratocystic odontogenic tumour and treatment modalities.
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Texto completo:
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Base de dados:
MEDLINE
Assunto principal:
Neoplasias Cutâneas
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Carcinoma Basocelular
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Síndrome do Nevo Basocelular
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Tumores Odontogênicos
Idioma:
En
Ano de publicação:
2024
Tipo de documento:
Article