A Case of Pan-TRK Positive Dermatofibrosarcoma Protuberans Located on the Nose.
Cureus
; 16(2): e54215, 2024 Feb.
Article
em En
| MEDLINE
| ID: mdl-38496071
ABSTRACT
Dermatofibrosarcoma protuberans (DFSP) is a rare and infiltrative soft tissue tumor. Our report details a distinctive case of DFSP with pan-TRK positivity in the right nasal dorsum of a 46-year-old female. Histological analysis identified NTRK fusion gene involvement in this patient, detectable through pan-TRK immunostaining. The case underscores the significance of comprehensive management for pan-TRK-positive DFSP in challenging facial locations, indicating the potential efficacy of TRK inhibitors.
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Base de dados:
MEDLINE
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En
Ano de publicação:
2024
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Article