An Overview of Hereditary Angioedema for the Primary Care Physician.
Med Clin North Am
; 108(4): 747-755, 2024 Jul.
Article
em En
| MEDLINE
| ID: mdl-38816115
ABSTRACT
Hereditary angioedema is a rare autosomal dominant condition characterized by episodes of swelling of the upper airway, intestines, and skin. The disorder is characterized by deficiency in C1 esterase inhibitor (C1-INH) or a decrease in functional C1-INH. Treatment options include on demand therapy (treatment of acute attacks), long-term prophylaxis, and short-term prophylaxis. Corticosteroids, epinephrine, and antihistamines are not effective for this form of angioedema. The high mortality in patients undiagnosed underscores a need for broader physician awareness to identify these patients and initiate therapy.
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Base de dados:
MEDLINE
Assunto principal:
Angioedemas Hereditários
Idioma:
En
Ano de publicação:
2024
Tipo de documento:
Article