ACTH-producing adrenocortical carcinoma: an exceedingly rare diagnosis.
J Egypt Natl Canc Inst
; 36(1): 24, 2024 Jul 15.
Article
em En
| MEDLINE
| ID: mdl-39004684
ABSTRACT
BACKGROUND:
Adrenocortical carcinoma is a very rare endocrinopathy that has a poor prognosis and is frequently associated with ACTH-independent Cushing's syndrome. Despite having an adrenocortical carcinoma, our patient surprisingly had an ACTH-dependent Cushing's syndrome. CASE REPORT A 26-year-old female presented with Cushing's syndrome and an abdominal mass. Imaging studies revealed an adrenal mass consistent with a high-grade malignancy. Laboratory workup showed hypercortisolism, hyperandrogenism, and hypokalemia with normal levels of metanephrines. Unexpectedly, her ACTH levels were remarkably elevated. The pathological analysis of a tumor sample was conclusive for adrenocortical carcinoma with immunopositivity for ACTH.CONCLUSIONS:
Our patient suffered from an adrenocortical carcinoma that was ectopically producing ACTH. This case emphasizes that physicians should have a broad-minded approach when evaluating cases of rare endocrine malignancies.Palavras-chave
Texto completo:
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Base de dados:
MEDLINE
Assunto principal:
Neoplasias do Córtex Suprarrenal
/
Carcinoma Adrenocortical
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Hormônio Adrenocorticotrópico
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Síndrome de Cushing
Idioma:
En
Ano de publicação:
2024
Tipo de documento:
Article