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1.
TTC19 Plays a Husbandry Role on UQCRFS1 Turnover in the Biogenesis of Mitochondrial Respiratory Complex III.
Mol Cell
; 67(1): 96-105.e4, 2017 Jul 06.
Article
in English
| MEDLINE | ID: mdl-28673544
2.
Double administration of self-complementary AAV9NDUFS4 prevents Leigh disease in Ndufs4-/- mice.
Brain
; 145(10): 3405-3414, 2022 10 21.
Article
in English
| MEDLINE | ID: mdl-36270002
3.
DNA polymerase gamma mutations that impair holoenzyme stability cause catalytic subunit depletion.
Nucleic Acids Res
; 49(9): 5230-5248, 2021 05 21.
Article
in English
| MEDLINE | ID: mdl-33956154
4.
Opa1 Overexpression Protects from Early-Onset Mpv17-/--Related Mouse Kidney Disease.
Mol Ther
; 28(8): 1918-1930, 2020 08 05.
Article
in English
| MEDLINE | ID: mdl-32562616
5.
Correction to 'DNA polymerase gamma mutations that impair holoenzyme stability cause catalytic subunit depletion'.
Nucleic Acids Res
; 49(18): 10803, 2021 Oct 11.
Article
in English
| MEDLINE | ID: mdl-34520541
6.
A Single Intravenous Injection of AAV-PHP.B-hNDUFS4 Ameliorates the Phenotype of Ndufs4 -/- Mice.
Mol Ther Methods Clin Dev
; 17: 1071-1078, 2020 Jun 12.
Article
in English
| MEDLINE | ID: mdl-32478122
7.
APOPT1/COA8 assists COX assembly and is oppositely regulated by UPS and ROS.
EMBO Mol Med
; 11(1)2019 01.
Article
in English
| MEDLINE | ID: mdl-30552096
8.
Rapamycin rescues mitochondrial myopathy via coordinated activation of autophagy and lysosomal biogenesis.
EMBO Mol Med
; 10(11)2018 11.
Article
in English
| MEDLINE | ID: mdl-30309855
9.
Perturbed Redox Signaling Exacerbates a Mitochondrial Myopathy.
Cell Metab
; 28(5): 764-775.e5, 2018 11 06.
Article
in English
| MEDLINE | ID: mdl-30122554
10.
Genome editing in mitochondria corrects a pathogenic mtDNA mutation in vivo.
Nat Med
; 24(11): 1691-1695, 2018 11.
Article
in English
| MEDLINE | ID: mdl-30250142
11.
Defective PITRM1 mitochondrial peptidase is associated with Aß amyloidotic neurodegeneration.
EMBO Mol Med
; 8(3): 176-90, 2016 Mar 01.
Article
in English
| MEDLINE | ID: mdl-26697887
12.
Opa1 overexpression ameliorates the phenotype of two mitochondrial disease mouse models.
Cell Metab
; 21(6): 845-54, 2015 Jun 02.
Article
in English
| MEDLINE | ID: mdl-26039449
13.
NAD(+)-dependent activation of Sirt1 corrects the phenotype in a mouse model of mitochondrial disease.
Cell Metab
; 19(6): 1042-9, 2014 Jun 03.
Article
in English
| MEDLINE | ID: mdl-24814483
14.
In vivo correction of COX deficiency by activation of the AMPK/PGC-1α axis.
Cell Metab
; 14(1): 80-90, 2011 Jul 06.
Article
in English
| MEDLINE | ID: mdl-21723506
15.
The ferredoxin-NADP+ reductase/ferredoxin electron transfer system of Plasmodium falciparum.
FEBS J
; 276(14): 3825-36, 2009 Jul.
Article
in English
| MEDLINE | ID: mdl-19523113
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