Your browser doesn't support javascript.
loading
Mostrar: 20 | 50 | 100
Resultados 1 - 1 de 1
Filtrar
Más filtros

Banco de datos
Tipo del documento
País de afiliación
Intervalo de año de publicación
1.
Genes (Basel) ; 15(7)2024 Jul 12.
Artículo en Inglés | MEDLINE | ID: mdl-39062689

RESUMEN

Structural variation is a source of genetic variation that, in some cases, may trigger pathogenicity. Here, we describe two cases, a mother and son, with the same partial inverted duplication of the long arm of chromosome 8 [invdup(8)(q24.21q24.21)] of 17.18 Mb, showing different clinical manifestations: microcephaly, dorsal hypertrichosis, seizures and neuropsychomotor development delay in the child, and a cleft lip/palate, down-slanted palpebral fissures and learning disabilities in the mother. The deleterious outcome, in general, is reflected by the gain or loss of genetic material. However, discrepancies among the clinical manifestations raise some concerns about the genomic configuration within the chromosome and other genetic modifiers. With that in mind, we also performed a literature review of research published in the last 20 years about the duplication of the same, or close, chromosome region, seeking the elucidation of at least some relevant clinical features.


Asunto(s)
Cromosomas Humanos Par 8 , Humanos , Femenino , Masculino , Cromosomas Humanos Par 8/genética , Adulto , Inversión Cromosómica/genética , Microcefalia/genética , Microcefalia/patología , Duplicación Cromosómica/genética , Niño , Preescolar
SELECCIÓN DE REFERENCIAS
DETALLE DE LA BÚSQUEDA