RESUMEN
A 4-year-old girl with PHACES syndrome (posterior fossa brain malformations, hemangiomas, arterial anomalies, cardiac anomalies/coarctation of the aorta, eye abnormalities, and sternal clefting/supraumbilical raphe) developed a cerebellar pilocytic astrocytoma 18 months after resolution of her neck, ear, and thoracic hemangiomas. Because cutaneous hemangiomas may have involuted by the time a patient is diagnosed with a central nervous system neoplasm, it seems possible that in other such patients the association may have gone unrecognized. Cerebellar pilocytic astrocytoma may be a rare manifestation of the posterior fossa malformations of PHACES.
Asunto(s)
Anomalías Múltiples , Astrocitoma/etiología , Encéfalo/anomalías , Hemangioma/complicaciones , Neoplasias Infratentoriales/etiología , Anomalías Múltiples/patología , Anomalías Múltiples/fisiopatología , Astrocitoma/patología , Encéfalo/patología , Preescolar , Femenino , Defectos del Tabique Interventricular/complicaciones , Hemangioma/congénito , Humanos , Neoplasias Infratentoriales/patología , Angiografía por Resonancia Magnética , Imagen por Resonancia Magnética , SíndromeRESUMEN
We report the first use of the Calypso system (Calypso Medical, Seattle, WA) in a pediatric patient with group III vaginal rhabdomyosarcoma. The Calypso system was used to improve patient setup, to limit anesthesia, to provide for real-time tracking of target location, and to minimize the need for daily portal imaging studies and their associated extraneous radiation dose.