RESUMO
Factor V deficiency is a congenital bleeding diathesis that, in selected cases, may be managed with liver transplant. In this case, we describe the treatment of an adult patient with kidney failure secondary to juvenile onset polycystic kidney disease who received a combined liver-kidney transplant as a method to manage the risks associated with the need for a kidney transplantin the setting of factorV deficiency and high sensitization.
Assuntos
Deficiência do Fator V , Transplante de Rim , Doenças Renais Policísticas , Adulto , Humanos , Transplante de Rim/efeitos adversos , Transplante de Rim/métodos , Deficiência do Fator V/complicações , Deficiência do Fator V/diagnóstico , Deficiência do Fator V/cirurgia , Resultado do Tratamento , Doenças Renais Policísticas/complicações , Doenças Renais Policísticas/diagnóstico , Doenças Renais Policísticas/genética , Rim , FígadoRESUMO
A young male suffered multiple severe injuries after a fall and near-drowning. On presentation to the emergency department (ED), he was in a critical and unstable condition and his chances of survival were deemed very low. This case illustrates the management of the hypothermic multi-trauma patient and the remarkable recovery made possible by a high standard of care.