[Myxoma of the mitral valve in a child. Apropos of an operated case]. / Myxome de la valve mitrale chez l'enfant. A propos d'un cas opéré.

The case of an 8 year old child with a symtomless murmur of mitral incompetence is reported. Echocardiography showed the presence of an intracardiac tumour, a mass of dense echos between the two mitral leaflets being recorded; multiscan examination suggested insertion on the anterior mitral leaflet. The tumour and its pedicle were resected, causing some loss of valvular tissue, which required repair with a strip of pericardium. This would appear to be the first reported case of mitral valve myxoma in children. Left atrial myxoma, the commonest cardiac tumour, is rarely observed before 15 years of age; insertion on the mitral valve itself is rare at any age. The site of insertion is determined by quite separate echocardiographic criteria compared to left atrial myxoma. This is important as surgery may sacrifice the mitral valve, and mitral valve replacement may be needed; valvuloplasty should be attempted in this age group, despite the risk of tumour recurrence, which is porbably greater with this unusual location.

[Orthostatic hypotension and obstructive hypertrophic cardiomyopathy (author's transl)]. / Hypotension orthostatique et cardiomyopathie obstructive.

The authors relate two cases of idiopathic hypertrophic subaortic stenosis detected after orthostatic hypotension with syncope. This type of detection has not been described till now. Relations between idiopathic hypertrophic subaortic stenosis and orthostatic hypotension are debated as well as relation between IHSS and systemic hypertension which has existed previously in the two cases. It seems suitable to call up IHSS systematically before every orthostatic hypotension at least in elderly. Beta-blockers can in such cases considerably improve orthostatic symptoms.

[Williams-Beuren syndrome and renovascular arterial hypertension]. / Syndrome de williams et beuren et hypertension artérielle réno-vasculaire.

The Williams and Beuren's syndrome associates a particuliar facies, a mental debility, a supravalvular aortic stenosis, and frequent vascular anomalies of pulmonary artery as well as aorta and its branches. Relations between this syndrome and congenital idiopathic hypercalcemia seem now determined; the hypertension which has been frequently observed in this last case, seems more unusual in the case of Williams and Beuren's syndrome. The authors report a case about this syndrome in which the hypertension seemed linked to a stenosis of the left renal artery and which has been treated surgically. A year later the result is satisfactory but the evolutive potential of arterial lesions described in this syndrome does not necessory lead to a final recovery. Besides there are in this disease hypertensions which are relevant to an other etiology (more especially aortic hypoplasia) and stenosis of renal arteries without hypertension.

[Severe cerebellar symdrome during aprindine treatment (author's transl)]. / Syndrome neurologique grave au cours d'un traitement par l'aprindine.

The authors, report a case of severe cerebellar syndrome, (preventory to remain standing) and connect with the dose of aprindine. This complication is coming with a little dose, facilitated with a minor renal insufficiency and a pre-existent neurologic disorder.