RESUMO
The management of children with organic acidemias (OAs) is limited in nursing literature. This article focuses on the two more common OAs, methylmalonic and propionic acidemias. Literature search was done on PUBMED, CINAHL, OVID, UptoDate, and GeneReview. The benefit of early diagnosis and treatment has been well documented, but many unresolved aspects of care management remain. Patient care is a complex necessitation and a lifelong follow-up for complications. Caring for patients with OA requires that nurses increase their familiarity with metabolic genetics and develop a better understanding of proper medical and nursing management while research continues to determine the most beneficial treatment and long-term care management methods.
Assuntos
Acidose/diagnóstico , Acidose/terapia , Erros Inatos do Metabolismo dos Aminoácidos/diagnóstico , Erros Inatos do Metabolismo dos Aminoácidos/terapia , Ácido Metilmalônico/metabolismo , Propionatos/metabolismo , Acidose/epidemiologia , Acidose/genética , Assistência ao Convalescente , Erros Inatos do Metabolismo dos Aminoácidos/epidemiologia , Erros Inatos do Metabolismo dos Aminoácidos/genética , Dieta com Restrição de Proteínas , Diagnóstico Precoce , Hidratação , Genes Recessivos/genética , Testes Genéticos , Hemofiltração , Humanos , Incidência , Recém-Nascido , Terapia Intensiva Neonatal , Transplante de Fígado , Enfermagem Neonatal , Triagem Neonatal , Papel do Profissional de Enfermagem , Avaliação em Enfermagem , Diagnóstico Pré-Natal , Taxa de SobrevidaRESUMO
Infiltration of a vesicant medication, defined as extravasation, may result in significant patient injuries. The first step in preventing extravasation is the identification and recognition of vesicant medications and solutions. Because there is no list of noncytotoxic vesicants as established by a professional organization, the Infusion Nurses Society, as the global authority in infusion nursing, identified the need to address this gap. A task force was formed for the purpose of creating an evidence-based list of noncytotoxic vesicant medications and solutions.