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Aquaporin 9 induction in human iPSC-derived hepatocytes facilitates modeling of ornithine transcarbamylase deficiency.
Laemmle, Alexander; Poms, Martin; Hsu, Bernadette; Borsuk, Mariia; Rüfenacht, Véronique; Robinson, Joshua; Sadowski, Martin C; Nuoffer, Jean-Marc; Häberle, Johannes; Willenbring, Holger.
Affiliation
  • Laemmle A; Eli and Edythe Broad Center of Regeneration Medicine and Stem Cell Research, University of California San Francisco, San Francisco, California, USA.
  • Poms M; Department of Pediatrics, University Children's Hospital, Bern, Switzerland.
  • Hsu B; University Institute of Clinical Chemistry, University of Bern, Bern, Switzerland.
  • Borsuk M; Division of Clinical Chemistry and Biochemistry, University Children's Hospital Zurich, Zurich, Switzerland.
  • Rüfenacht V; Eli and Edythe Broad Center of Regeneration Medicine and Stem Cell Research, University of California San Francisco, San Francisco, California, USA.
  • Robinson J; University Institute of Clinical Chemistry, University of Bern, Bern, Switzerland.
  • Sadowski MC; Division of Metabolism and Children`s Research Center, University Children's Hospital, Zurich, Switzerland.
  • Nuoffer JM; Eli and Edythe Broad Center of Regeneration Medicine and Stem Cell Research, University of California San Francisco, San Francisco, California, USA.
  • Häberle J; Center for Reproductive Sciences, University of California San Francisco, San Francisco, California, USA.
  • Willenbring H; Department of Obstetrics, Gynecology, and Reproductive Sciences, University of California San Francisco, San Francisco, California, USA.
Hepatology ; 76(3): 646-659, 2022 09.
Article in En | MEDLINE | ID: mdl-34786702

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Aquaporins / Ornithine Carbamoyltransferase Deficiency Disease / Induced Pluripotent Stem Cells / Liver Diseases Type of study: Prognostic_studies Limits: Adult / Humans Language: En Journal: Hepatology Year: 2022 Type: Article Affiliation country: United States

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Aquaporins / Ornithine Carbamoyltransferase Deficiency Disease / Induced Pluripotent Stem Cells / Liver Diseases Type of study: Prognostic_studies Limits: Adult / Humans Language: En Journal: Hepatology Year: 2022 Type: Article Affiliation country: United States