Keratocystic odontogenic tumor related to nevoid basal cell carcinoma syndrome: clinicopathological study
Braz. j. oral sci
; 12(1): 23-29, jan.-mar. 2013. ilus, tab
Article
en En
| LILACS, BBO
| ID: lil-671928
Biblioteca responsable:
BR97.1
ABSTRACT
Aim:
To assess clinicopathological features of patients with keratocystic odontogenic tumor (KCOT) associated with nevoid basal cell carcinoma syndrome (NBCCS) in a single Brazilian institution.Methods:
After histopathological analyses of KCOT related to NBCCS, the medical charts of 14 patients were assessed. These patients presented a total of 31 primary and 8 recurrent KCOT.Results:
Out of 14 patients, 8 presented a single KCOT, 4 showed synchronous tumors, 1 had3 metachronous lesions and another patient had 2 synchronous lesions at initial evaluation and then developed other 3 metachronous lesions. Besides the 31 primary KCOTs, 18 lesions were located in mandible and 13 in maxilla. Most tumors presented unilocular pattern and association with a tooth.Conclusions:
KCOT is a frequent manifestation of NBCCS and can be its first sign, mainly in young patients. In contrast to a previously published series, most patients presented a single lesion.
Texto completo:
1
Colección:
01-internacional
Banco de datos:
BBO
/
LILACS
Asunto principal:
Carcinoma
/
Síndrome del Nevo Basocelular
Límite:
Female
/
Humans
/
Male
Idioma:
En
Revista:
Braz. j. oral sci
/
Brazilian journal of oral sciences (Impresso)
/
Brazilian journal of oral sciences (Online)
Asunto de la revista:
ODONTOLOGIA
Año:
2013
Tipo del documento:
Article
País de afiliación:
Brasil