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Long-chain acyl-CoA dehydrogenase deficiency as a cause of pulmonary surfactant dysfunction.
Goetzman, Eric S; Alcorn, John F; Bharathi, Sivakama S; Uppala, Radha; McHugh, Kevin J; Kosmider, Beata; Chen, Rimei; Zuo, Yi Y; Beck, Megan E; McKinney, Richard W; Skilling, Helen; Suhrie, Kristen R; Karunanidhi, Anuradha; Yeasted, Renita; Otsubo, Chikara; Ellis, Bryon; Tyurina, Yulia Y; Kagan, Valerian E; Mallampalli, Rama K; Vockley, Jerry.
Afiliación
  • Goetzman ES; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224; Department of Human Genetics, Graduate School of Public Health, University of Pittsburgh, Pittsburgh, Pennsylvania
  • Alcorn JF; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • Bharathi SS; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • Uppala R; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • McHugh KJ; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • Kosmider B; Department of Medicine, National Jewish Health, Denver, Colorado 80206.
  • Chen R; Department of Mechanical Engineering, University of Hawaii at Manoa, Honolulu, Hawaii 96822.
  • Zuo YY; Department of Mechanical Engineering, University of Hawaii at Manoa, Honolulu, Hawaii 96822.
  • Beck ME; Department of Human Genetics, Graduate School of Public Health, University of Pittsburgh, Pittsburgh, Pennsylvania 15213.
  • McKinney RW; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • Skilling H; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • Suhrie KR; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • Karunanidhi A; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • Yeasted R; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • Otsubo C; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224.
  • Ellis B; Department of Medicine, Acute Lung Injury Center of Excellence, University of Pittsburgh, Pittsburgh, Pennsylvania 15213.
  • Tyurina YY; Center for Free Radical and Antioxidant Health, University of Pittsburgh, Pittsburgh, Pennsylvania 15260; Department of Environmental and Occupational Health, University of Pittsburgh, Pittsburgh, Pennsylvania 15260.
  • Kagan VE; Center for Free Radical and Antioxidant Health, University of Pittsburgh, Pittsburgh, Pennsylvania 15260; Department of Environmental and Occupational Health, University of Pittsburgh, Pittsburgh, Pennsylvania 15260.
  • Mallampalli RK; Department of Medicine, Acute Lung Injury Center of Excellence, University of Pittsburgh, Pittsburgh, Pennsylvania 15213; Medical Specialty Service Line, Veterans Affairs Pittsburgh Healthcare System, Pittsburgh, Pennsylvania 15213.
  • Vockley J; Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh of University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania 15224; Department of Human Genetics, Graduate School of Public Health, University of Pittsburgh, Pittsburgh, Pennsylvania
J Biol Chem ; 289(15): 10668-10679, 2014 Apr 11.
Article en En | MEDLINE | ID: mdl-24591516

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Surfactantes Pulmonares / Acil-CoA Deshidrogenasa de Cadena Larga / Errores Innatos del Metabolismo Lipídico / Enfermedades Pulmonares Tipo de estudio: Prognostic_studies Límite: Adult / Animals / Female / Humans / Infant / Male / Newborn Idioma: En Revista: J Biol Chem Año: 2014 Tipo del documento: Article

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Surfactantes Pulmonares / Acil-CoA Deshidrogenasa de Cadena Larga / Errores Innatos del Metabolismo Lipídico / Enfermedades Pulmonares Tipo de estudio: Prognostic_studies Límite: Adult / Animals / Female / Humans / Infant / Male / Newborn Idioma: En Revista: J Biol Chem Año: 2014 Tipo del documento: Article