[Splenectomy in Gaucher's disease. Apropos of 2 cases, one of which was preceded by embolization]. / La splénectomie dans la maladie de Gaucher. A propos de deux cas dont l'un précédé d'une embolisation.

ABSTRACT

Two cases of Gaucher's disease type I are reported Splenectomy was indicated because of hypersplenism and massive splenomegaly. In one case hypersplenism was treated with pre-operative selective embolization because of the volume of the spleen (20 kg). The embolization corrected the thrombopenia but not the size of the spleen. Four years after operation for case 1 and eight months for case two, there is an improvement in the clinical status.