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Severe Pulmonary Fibrosis as the First Manifestation of Interferonopathy (TMEM173 Mutation).
Picard, Cécile; Thouvenin, Guillaume; Kannengiesser, Caroline; Dubus, Jean-Christophe; Jeremiah, Nadia; Rieux-Laucat, Frédéric; Crestani, Bruno; Belot, Alexandre; Thivolet-Béjui, Françoise; Secq, Véronique; Ménard, Christelle; Reynaud-Gaubert, Martine; Reix, Philippe.
Afiliación
  • Picard C; Department of Pathology, Hôpital Femme-Mère-Enfant, Hospices civils de Lyon, Claude Bernard Lyon 1 University, Lyon, France; Inserm U1111, Lyon, France.
  • Thouvenin G; Pediatric Pulmonology Department, Assistance publique-Hôpitaux de Paris, Hôpital Armand Trousseau, Paris, France; Inserm U938, Hôpital Saint-Antoine, Paris, France.
  • Kannengiesser C; Department of Genetic, Assistance publique-Hôpitaux de Paris, Hôpital Bichat, Université Paris Diderot, Paris, France.
  • Dubus JC; Pediatric Pulmonology Department, Assistance publique-Hôpitaux de Marseille, Hôpital de la Timone, Marseille, France.
  • Jeremiah N; Institut Imagine, Hôpital Necker, Paris, France.
  • Rieux-Laucat F; Institut Imagine, Hôpital Necker, Paris, France.
  • Crestani B; Inserm U1152, Université de Paris Diderot, Paris, France.
  • Belot A; Inserm U1111, Lyon, France; Pediatric Rheumatology, Nephrology and Dermatology Department, Hôpital Femme-Mère-Enfant, Hospices civils de Lyon, Lyon, France.
  • Thivolet-Béjui F; Department of Pathology, Hôpital Femme-Mère-Enfant, Hospices civils de Lyon, Claude Bernard Lyon 1 University, Lyon, France.
  • Secq V; Department of Pathology, Assistance publique-Hôpitaux de Marseille, Hôpital de la Timone, Marseille, France.
  • Ménard C; Pediatric Pulmonology Department, Assistance publique-Hôpitaux de Paris, Hôpital Armand Trousseau, Paris, France.
  • Reynaud-Gaubert M; Pulmonology Department, CHU Nord, Assistance publique-Hôpitaux de Marseille, Université de la Méditerranée, Marseille, France.
  • Reix P; Pediatric Pulmonology Department, Hôpital Femme-Mère-Enfant, Hospices civils de Lyon, UMR5558, Lyon, France. Electronic address: philippe.reix@chu-lyon.fr.
Chest ; 150(3): e65-71, 2016 Sep.
Article en En | MEDLINE | ID: mdl-27613991

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Fibrosis Pulmonar / Enfermedades Autoinmunes / Inflamación / Proteínas de la Membrana / Mutación Límite: Adult / Child / Female / Humans / Infant / Male Idioma: En Revista: Chest Año: 2016 Tipo del documento: Article País de afiliación: Francia

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Fibrosis Pulmonar / Enfermedades Autoinmunes / Inflamación / Proteínas de la Membrana / Mutación Límite: Adult / Child / Female / Humans / Infant / Male Idioma: En Revista: Chest Año: 2016 Tipo del documento: Article País de afiliación: Francia