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4-PBA ameliorates cellular homeostasis in fibroblasts from osteogenesis imperfecta patients by enhancing autophagy and stimulating protein secretion.
Besio, Roberta; Iula, Giusy; Garibaldi, Nadia; Cipolla, Lina; Sabbioneda, Simone; Biggiogera, Marco; Marini, Joan C; Rossi, Antonio; Forlino, Antonella.
Afiliación
  • Besio R; Department of Molecular Medicine, Biochemistry Unit, University of Pavia, Pavia 27100, Italy. Electronic address: roberta.besio@unipv.it.
  • Iula G; Department of Molecular Medicine, Biochemistry Unit, University of Pavia, Pavia 27100, Italy. Electronic address: giusy.iula01@universitadipavia.it.
  • Garibaldi N; Department of Molecular Medicine, Biochemistry Unit, University of Pavia, Pavia 27100, Italy. Electronic address: nadia.garibaldi01@universitadipavia.it.
  • Cipolla L; Istituto di Genetica Molecolare, Consiglio Nazionale delle Ricerche, Pavia 27100, Italy. Electronic address: lina.cipolla@igm.cnr.it.
  • Sabbioneda S; Istituto di Genetica Molecolare, Consiglio Nazionale delle Ricerche, Pavia 27100, Italy. Electronic address: simone.sabbioneda@igm.cnr.it.
  • Biggiogera M; Department of Biology and Biotechnology, University of Pavia, 27100 Pavia, Italy. Electronic address: marco.biggiogera@unipv.it.
  • Marini JC; Bone and Extracellular Matrix Branch, NICHD, National Institute of Health, Bethesda, MD 20892, USA. Electronic address: marinij@mail.nih.gov.
  • Rossi A; Department of Molecular Medicine, Biochemistry Unit, University of Pavia, Pavia 27100, Italy. Electronic address: antrossi@unipv.it.
  • Forlino A; Department of Molecular Medicine, Biochemistry Unit, University of Pavia, Pavia 27100, Italy. Electronic address: aforlino@unipv.it.
Biochim Biophys Acta Mol Basis Dis ; 1864(5 Pt A): 1642-1652, 2018 May.
Article en En | MEDLINE | ID: mdl-29432813

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Osteogénesis Imperfecta / Fenilbutiratos / Autofagia / Fibroblastos / Homeostasis Límite: Humans Idioma: En Revista: Biochim Biophys Acta Mol Basis Dis Año: 2018 Tipo del documento: Article

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Osteogénesis Imperfecta / Fenilbutiratos / Autofagia / Fibroblastos / Homeostasis Límite: Humans Idioma: En Revista: Biochim Biophys Acta Mol Basis Dis Año: 2018 Tipo del documento: Article