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Paroxysmal nocturnal hemoglobinuria and vascular liver disease: Eculizumab therapy decreases mortality and thrombotic complications.
Plessier, Aurélie; Esposito-Farèse, Marina; Baiges, Anna; Shukla, Akash; Garcia Pagan, Juan Carlos; De Raucourt, Emmanuelle; Ollivier-Hourmand, Isabelle; Cervoni, Jean-Paul; De Ledinghen, Victor; Tazi, Zoubida; Nousbaum, Jean-Baptiste; Bun, René; Bureau, Christophe; Silvain, Christine; Tournilhac, Olivier; Gerfaud-Valentin, Mathieu; Durand, François; Goria, Odile; Tellez, Luis; Albillos, Agustin; Gioia, Stefania; Riggio, Oliviero; De Gottardi, Andrea; Payance, Audrey; Rautou, Pierre-Emmanuel; Terriou, Louis; Charbonnier, Aude; Elkrief, Laure; de la Tour, Regis Peffault; Valla, Dominique-Charles; Gault, Nathalie; de Fontbrune, Flore Sicre.
Afiliación
  • Plessier A; Université de Paris, AP-HP, Hôpital Beaujon, Service d'Hépatologie, DMU DIGEST, Centre de Référence des Maladies Vasculaires du Foie, FILFOIE, ERN RARE-LIVER, Centre de recherche sur l'inflammation, Inserm, UMR 1149, Paris, France.
  • Esposito-Farèse M; Unité de Recherche Clinique, Hôpital Bichat, AP-HP. Nord, Université de Paris, Paris, France.
  • Baiges A; INSERM CIC-EC 1425, AP-HP. Nord - Université de Paris, Paris, France.
  • Shukla A; Barcelona Hepatic Hemodynamic Laboratory, Liver Unit, Hospital Clínic, IDIBAPS, University of Barcelona, Health Care Provider of the ERN-Liver, Centro de Investigación Biomédica Red de Enfermedades Hepáticas y Digestivas (CIBEREHD), Barcelona, Spain.
  • Garcia Pagan JC; Department of Gastroenterology, Seth GS Medical College & KEM Hospital, Mumbai, India.
  • De Raucourt E; Barcelona Hepatic Hemodynamic Laboratory, Liver Unit, Hospital Clínic, IDIBAPS, University of Barcelona, Health Care Provider of the ERN-Liver, Centro de Investigación Biomédica Red de Enfermedades Hepáticas y Digestivas (CIBEREHD), Barcelona, Spain.
  • Ollivier-Hourmand I; Department of Laboratory Hematology, Hôpital Beaujon, APHP Nord Université de Paris, Clichy, France.
  • Cervoni JP; Department of Gastroenterology and Hepatology, Côte de la Nacre Hospital, University Hospital of Caen, Caen Cedex 9, France.
  • De Ledinghen V; Department of Hepatology and Intensive Digestive Care, Jean Minjoz Hospital, Besançon, France.
  • Tazi Z; Department of Hepatology and INSERMU1053, Haut-Lévêque Hospital, University Hospital of Bordeaux, Pessac, France.
  • Nousbaum JB; Internal Medicine, Mohammed V University Ibn Sina hospital, Rabat, Morocco.
  • Bun R; Department of Gastroenterology and Hepatology, Brest hospital, Brest, France.
  • Bureau C; Unité de Recherche Clinique, Hôpital Bichat, AP-HP. Nord, Université de Paris, Paris, France.
  • Silvain C; INSERM CIC-EC 1425, AP-HP. Nord - Université de Paris, Paris, France.
  • Tournilhac O; Department of Gastroenterology and Hepatology, Rangueil Hospital, University Hospital of Toulouse, Toulouse, France.
  • Gerfaud-Valentin M; Department of Gastroenterology and Hepatology, University Hospital of Poitiers, Poitiers, France.
  • Durand F; Department of hematology, Estaing Hostpital, University Hospital of Clermont-Ferrand, Clermont-Ferrand Cedex 1, France.
  • Goria O; Department of Internal Medicine, Hôpital de la croix Rousse, Lyon, France.
  • Tellez L; Université de Paris, AP-HP, Hôpital Beaujon, Service d'Hépatologie, DMU DIGEST, Centre de Référence des Maladies Vasculaires du Foie, FILFOIE, ERN RARE-LIVER, Centre de recherche sur l'inflammation, Inserm, UMR 1149, Paris, France.
  • Albillos A; Gastroenterology and Hepatology department, Charles Nicolle Hospital, University Hospital of Rouen, Rouen, France.
  • Gioia S; Department of Gastroenterology and Hepatology, Hospital Ramón y Cajal Madrid, IRYCIS, Madrid, Spain.
  • Riggio O; Universidad de Alcalá, Madrid, Spain.
  • De Gottardi A; Department of Gastroenterology and Hepatology, Hospital Ramón y Cajal Madrid, IRYCIS, Madrid, Spain.
  • Payance A; Universidad de Alcalá, Madrid, Spain.
  • Rautou PE; Department of Translational and Precision Medicine, Sapienza University of Rome, Rome, Italy.
  • Terriou L; Department of Translational and Precision Medicine, Sapienza University of Rome, Rome, Italy.
  • Charbonnier A; Inselspital, Bern, and Servizio di Gastroenterologia e Epatologia, Ente Ospedaliero Cantonale and Faculty of Biomedical Sciences, Università della Svizzera italiana, Lugano, Switzerland.
  • Elkrief L; Université de Paris, AP-HP, Hôpital Beaujon, Service d'Hépatologie, DMU DIGEST, Centre de Référence des Maladies Vasculaires du Foie, FILFOIE, ERN RARE-LIVER, Centre de recherche sur l'inflammation, Inserm, UMR 1149, Paris, France.
  • de la Tour RP; Université de Paris, AP-HP, Hôpital Beaujon, Service d'Hépatologie, DMU DIGEST, Centre de Référence des Maladies Vasculaires du Foie, FILFOIE, ERN RARE-LIVER, Centre de recherche sur l'inflammation, Inserm, UMR 1149, Paris, France.
  • Valla DC; Hematology Department, CHU Lille, Hôpital Claude Huriez, Lille, France.
  • Gault N; Hematology Unit, Institut Paoli Calmettes, Marseille, France.
  • de Fontbrune FS; CHU de Tours, Hepatogastroenterology Unit, Hôpital Trousseau, Tours Cedex 9, France.
Am J Hematol ; 97(4): 431-439, 2022 04.
Article en En | MEDLINE | ID: mdl-35049058

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Trombosis / Hemoglobinuria Paroxística / Hepatopatías Tipo de estudio: Observational_studies / Risk_factors_studies Límite: Adult / Female / Humans / Male Idioma: En Revista: Am J Hematol Año: 2022 Tipo del documento: Article País de afiliación: Francia

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Trombosis / Hemoglobinuria Paroxística / Hepatopatías Tipo de estudio: Observational_studies / Risk_factors_studies Límite: Adult / Female / Humans / Male Idioma: En Revista: Am J Hematol Año: 2022 Tipo del documento: Article País de afiliación: Francia