[Pseudoxanthoma elasticum]. / Pseudoxantoma elástico.

ABSTRACT

Four young female patients with Pseudodixanthome elasticum are reported, corresponding to the Grönblad and Strandberg syndrome. The dysplastic derangement of the elastic fibers with a potentially systemic compromise is considered, which explains the multiorganic character of the disease. We conferred to the skin changes the means of a marker that obligates an exhaustive study and follow-up of the patients to make visceral affectations.