Perivascular epithelioid cell tumour-mimicking retroperitoneal leiomyosarcoma.
BMJ Case Rep
; 15(8)2022 Aug 19.
Article
en En
| MEDLINE
| ID: mdl-35985749
ABSTRACT
A young man in his 40s was evaluated in the emergency department for abdominal and right flank pain. A CT scan of the abdomen and pelvis showed a solid, well-circumscribed lesion measuring 7.1×8.1×5.4 cm, which was arising from the retroperitoneum and extending from the third portion of the duodenum towards the right kidney. A percutaneous core biopsy was obtained, demonstrating an atypical smooth muscle neoplasm suggestive of a low-grade leiomyosarcoma. The patient underwent surgery for an en-block resection of the mass and the final pathology confirmed a perivascular epithelioid cell neoplasm without significant pleomorphism, mitosis or necrosis. Our case adds to the small number of perivascular epithelioid cell tumour cases reported in the literature and we present it in order to increase our understanding of this tumour and to assist in its appropriate diagnosis and management.
Palabras clave
Texto completo:
1
Colección:
01-internacional
Banco de datos:
MEDLINE
Asunto principal:
Neoplasias Retroperitoneales
/
Neoplasias de Células Epitelioides Perivasculares
/
Leiomiosarcoma
Límite:
Humans
/
Male
Idioma:
En
Revista:
BMJ Case Rep
Año:
2022
Tipo del documento:
Article
País de afiliación:
Estados Unidos