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A missense mutation in the proprotein convertase gene furinb causes hepatic cystogenesis during liver development in zebrafish.
Ellis, Jillian L; Evason, Kimberley J; Zhang, Changwen; Fourman, Makenzie N; Liu, Jiandong; Ninov, Nikolay; Delous, Marion; Vanhollebeke, Benoit; Fiddes, Ian; Otis, Jessica P; Houvras, Yariv; Farber, Steven A; Xu, Xiaolei; Lin, Xueying; Stainier, Didier Y R; Yin, Chunyue.
Afiliación
  • Ellis JL; Division of Gastroenterology, Hepatology, and Nutrition, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.
  • Evason KJ; Department of Biochemistry and Biophysics, Program in Developmental and Stem Cell Biology, Liver Center and Diabetes Center, University of California, San Francisco, San Francisco, California, USA.
  • Zhang C; Huntsman Cancer Institute and Department of Pathology, University of Utah, Salt Lake City, Utah, USA.
  • Fourman MN; Division of Gastroenterology, Hepatology, and Nutrition, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.
  • Liu J; Division of Gastroenterology, Hepatology, and Nutrition, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.
  • Ninov N; Department of Biochemistry and Biophysics, Program in Developmental and Stem Cell Biology, Liver Center and Diabetes Center, University of California, San Francisco, San Francisco, California, USA.
  • Delous M; McAllister Heart Institute, Department of Pathology and Laboratory Medicine, School of Medicine, The University of North Carolina at Chapel Hill, Chapel Hill, North Carolina, USA.
  • Vanhollebeke B; Department of Biochemistry and Biophysics, Program in Developmental and Stem Cell Biology, Liver Center and Diabetes Center, University of California, San Francisco, San Francisco, California, USA.
  • Fiddes I; Center for Regenerative Therapies TU Dresden, Dresden, Germany.
  • Otis JP; Paul Langerhans Institute Dresden of the Helmholtz Center Munich at the University Hospital Carl Gustav Carus of TU Dresden, German Center for Diabetes Research, Dresden, Germany.
  • Houvras Y; Department of Biochemistry and Biophysics, Program in Developmental and Stem Cell Biology, Liver Center and Diabetes Center, University of California, San Francisco, San Francisco, California, USA.
  • Farber SA; Equipe GENDEV, Centre de Recherche en Neurosciences de Lyon, Inserm U1028, CNRS UMR5292, Universite Lyon 1, Universite St Etienne, Lyon, France.
  • Xu X; Department of Biochemistry and Biophysics, Program in Developmental and Stem Cell Biology, Liver Center and Diabetes Center, University of California, San Francisco, San Francisco, California, USA.
  • Lin X; Laboratory of Neurovascular Signaling, Department of Molecular Biology, ULB Neuroscience Institute, Universite Libre de Bruxelles, Gosselies, Belgium.
  • Stainier DYR; Department of Biochemistry and Biophysics, Program in Developmental and Stem Cell Biology, Liver Center and Diabetes Center, University of California, San Francisco, San Francisco, California, USA.
  • Yin C; Department of Embryology, Carnegie Institution for Science, Baltimore, Maryland, USA.
Hepatol Commun ; 6(11): 3083-3097, 2022 11.
Article en En | MEDLINE | ID: mdl-36017776

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Pez Cebra / Quistes Tipo de estudio: Etiology_studies Límite: Animals Idioma: En Revista: Hepatol Commun Año: 2022 Tipo del documento: Article País de afiliación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Pez Cebra / Quistes Tipo de estudio: Etiology_studies Límite: Animals Idioma: En Revista: Hepatol Commun Año: 2022 Tipo del documento: Article País de afiliación: Estados Unidos