Plastic bronchitis as an unusual cause of mucus plugging in cystic fibrosis.
Pediatr Pulmonol
; 44(9): 939-40, 2009 Sep.
Article
em En
| MEDLINE
| ID: mdl-19658112
ABSTRACT
Cystic fibrosis patients are known to produce abundant, purulent sputum consisting mainly of DNA and cellular debris. We present a case of a CF patient with recurrent airway obstruction caused by a rare condition known as plastic bronchitis (PB). PB is characterized by the formation of casts of the airways that cause obstruction. Multiple etiologies have been proposed, but to our knowledge, no CF patient has been reported in any PB classification. Histological analysis and in-vitro testing of the cast were important factors in choosing the adequate therapy in this patient.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Acetilcisteína
/
Bronquite
/
Fibrose Cística
/
Doença Pulmonar Obstrutiva Crônica
/
Expectorantes
Tipo de estudo:
Etiology_studies
Limite:
Child, preschool
/
Humans
/
Male
Idioma:
En
Revista:
Pediatr Pulmonol
Assunto da revista:
PEDIATRIA
Ano de publicação:
2009
Tipo de documento:
Article
País de afiliação:
Canadá