Sinonasal adenocarcinoma: a rare second malignancy in long term retinoblastoma survivors.
Pediatr Blood Cancer
; 57(4): 693-5, 2011 Oct.
Article
em En
| MEDLINE
| ID: mdl-21548012
ABSTRACT
Retinoblastoma is the most common primary cancer of the eye in children. The incidence of second tumors in survivors of bilateral retinoblastoma and in survivors of unilateral retinoblastoma who presumably carry a germline RB1 mutation is documented. This article describes the previously unrecognized association of sinonasal adenocarcinoma as a second malignancy in retinoblastoma survivors. We present three cases who received radiation therapy as a part of their treatment and developed sinonasal adenocarcinoma as a second malignancy. Sinonasal adenocarcinoma should be considered as a second malignancy in retinoblastoma survivors who present with vague sinus symptoms.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Retinoblastoma
/
Neoplasias dos Seios Paranasais
/
Adenocarcinoma
/
Neoplasias Nasais
/
Segunda Neoplasia Primária
/
Neoplasias Induzidas por Radiação
Tipo de estudo:
Etiology_studies
Limite:
Adult
/
Aged
/
Humans
/
Male
/
Middle aged
/
Newborn
Idioma:
En
Revista:
Pediatr Blood Cancer
Assunto da revista:
HEMATOLOGIA
/
NEOPLASIAS
/
PEDIATRIA
Ano de publicação:
2011
Tipo de documento:
Article
País de afiliação:
Estados Unidos