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Impaired Lysosomal Function Underlies Monoclonal Light Chain-Associated Renal Fanconi Syndrome.
Luciani, Alessandro; Sirac, Christophe; Terryn, Sara; Javaugue, Vincent; Prange, Jenny Ann; Bender, Sébastien; Bonaud, Amélie; Cogné, Michel; Aucouturier, Pierre; Ronco, Pierre; Bridoux, Frank; Devuyst, Olivier.
Afiliação
  • Luciani A; Institute of Physiology, Zurich Center for Integrative Human Physiology, University of Zurich, Zurich, Switzerland;
  • Sirac C; Department of Immunology, National Center for Scientific Research, Joint Research Unit 7276, University of Limoges, Limoges, France; National Reference Center for Amyloidosis and other Monoclonal Immunoglobulin Deposition Diseases, University Hospital of Limoges, Poitiers, France;
  • Terryn S; Division of Nephrology, UCL Medical School, Brussels, Belgium;
  • Javaugue V; Department of Immunology, National Center for Scientific Research, Joint Research Unit 7276, University of Limoges, Limoges, France; Department of Nephrology, University Hospital, Poitiers University, Poitiers, France;
  • Prange JA; Institute of Physiology, Zurich Center for Integrative Human Physiology, University of Zurich, Zurich, Switzerland;
  • Bender S; Department of Immunology, National Center for Scientific Research, Joint Research Unit 7276, University of Limoges, Limoges, France; Department of Nephrology, University Hospital, Poitiers University, Poitiers, France;
  • Bonaud A; Department of Immunology, National Center for Scientific Research, Joint Research Unit 7276, University of Limoges, Limoges, France;
  • Cogné M; Department of Immunology, National Center for Scientific Research, Joint Research Unit 7276, University of Limoges, Limoges, France;
  • Aucouturier P; Department of Immunology, National Institute of Health and Medical Research Unit 938, Saint Antoine Hospital, Pierre et Marie Curie University, Paris, France;
  • Ronco P; Department of Nephrology and Dialysis, Tenon Hospital, Paris, France; Department of Immunology, National Institute of Health and Medical Research Unit 938, Saint Antoine Hospital, Pierre et Marie Curie University, Department of Nephrology and Dialysis, Tenon Hospital, Paris, France; Sorbonne Univers
  • Bridoux F; Department of Immunology, National Center for Scientific Research, Joint Research Unit 7276, University of Limoges, Limoges, France; Department of Nephrology, University Hospital, Poitiers University, Poitiers, France; f.bridoux@chu-poitiers.fr olivier.devuyst@uzh.ch.
  • Devuyst O; Institute of Physiology, Zurich Center for Integrative Human Physiology, University of Zurich, Zurich, Switzerland; Division of Nephrology, UCL Medical School, Brussels, Belgium; f.bridoux@chu-poitiers.fr olivier.devuyst@uzh.ch.
J Am Soc Nephrol ; 27(7): 2049-61, 2016 07.
Article em En | MEDLINE | ID: mdl-26614382

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Paraproteinemias / Cadeias Leves de Imunoglobulina / Síndrome de Fanconi / Lisossomos Tipo de estudo: Risk_factors_studies Limite: Animals Idioma: En Revista: J Am Soc Nephrol Assunto da revista: NEFROLOGIA Ano de publicação: 2016 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Paraproteinemias / Cadeias Leves de Imunoglobulina / Síndrome de Fanconi / Lisossomos Tipo de estudo: Risk_factors_studies Limite: Animals Idioma: En Revista: J Am Soc Nephrol Assunto da revista: NEFROLOGIA Ano de publicação: 2016 Tipo de documento: Article