Congenital ciliary aplasia in two siblings. A primitive disregulation of ciliogenesis?
Pathol Res Pract
; 185(2): 181-3, 1989 Aug.
Article
em En
| MEDLINE
| ID: mdl-2798216
ABSTRACT
Congenital ciliary aplasia was demonstrated in two siblings with clinical history of primary ciliary dyskinesia. Ultrastructural histochemistry of successive bronchial biopsies revealed the predominance of immature mucous cells and the total absence of ciliated or preciliated cells in the respiratory epithelium. This original disorder may represent a unique variant of primary ciliary dyskinesia with primitive disregulation of ciliogenesis.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Brônquios
/
Broncopatias
/
Transtornos da Motilidade Ciliar
Tipo de estudo:
Diagnostic_studies
Limite:
Child
/
Female
/
Humans
/
Male
Idioma:
En
Revista:
Pathol Res Pract
Ano de publicação:
1989
Tipo de documento:
Article
País de afiliação:
França