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Management of cholestatic pruritus in children with Alagille syndrome: Case report and literature review.
Ben Ameur, S; Chabchoub, I; Telmoudi, J; Belfitouri, Y; Rebah, O; Lacaille, F; Aloulou, H; Mehrzi, A; Hachicha, M.
Afiliação
  • Ben Ameur S; Pediatric department, Hedi Chaker Hospital, El ain street km 0,5, 3029 Sfax, Tunisia; Faculty of medicine, university of Sfax, Tunisia. Electronic address: benameursalma@gmail.com.
  • Chabchoub I; Pediatric department, Hedi Chaker Hospital, El ain street km 0,5, 3029 Sfax, Tunisia.
  • Telmoudi J; Pediatric department, Hedi Chaker Hospital, El ain street km 0,5, 3029 Sfax, Tunisia.
  • Belfitouri Y; Pediatric department, Hedi Chaker Hospital, El ain street km 0,5, 3029 Sfax, Tunisia.
  • Rebah O; Pediatric department, La Marsa Hospital, Tunis, Tunisia.
  • Lacaille F; Hepatogastroenterology-nutrition unit, Hôpital Necker-Enfants-Malades, 149, rue de Sèvres, 75015 Paris, France.
  • Aloulou H; Pediatric department, Hedi Chaker Hospital, El ain street km 0,5, 3029 Sfax, Tunisia.
  • Mehrzi A; Pediatric department, La Marsa Hospital, Tunis, Tunisia.
  • Hachicha M; Pediatric department, Hedi Chaker Hospital, El ain street km 0,5, 3029 Sfax, Tunisia.
Arch Pediatr ; 23(12): 1247-1250, 2016 Dec.
Article em En | MEDLINE | ID: mdl-28492167
ABSTRACT
Alagille syndrome causes intractable pruritus and disfiguring xanthomas because of retained bile acids and cholesterol. Drug therapy in addition to surgical intervention may be effective in many patients in reducing serum bile acids, cholesterol levels, pruritus, and skin xanthomas. In this report, we describe a child with Alagille syndrome who presented with severe pruritus and xanthomas as a consequence of severe hypercholesterolemia and discuss the treatment modalities.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Prurido / Xantomatose / Colestase / Síndrome de Alagille Limite: Child / Humans / Male Idioma: En Revista: Arch Pediatr Ano de publicação: 2016 Tipo de documento: Article
Texto completo
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Prurido / Xantomatose / Colestase / Síndrome de Alagille Limite: Child / Humans / Male Idioma: En Revista: Arch Pediatr Ano de publicação: 2016 Tipo de documento: Article