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Chronic Cholangiopathy Associated with Primary Immune Deficiencies Can Be Resolved by Effective Hematopoietic Stem Cell Transplantation.
Hadzic, Nedim; Nademi, Zohreh; Deheragoda, Maesha; Zen, Yoh; Elfeky, Reem; Worth, Austen; Veys, Paul; Mieli-Vergani, Giorgina; Davies, E Graham.
Afiliação
  • Hadzic N; Pediatric Liver Center for Hepatology, Gastroenterology, and Nutrition, King's College Hospital, London, United Kingdom; Institute of Liver Studies, MowatLabs, King's College Hospital, London, United Kingdom. Electronic address: nedim.hadzic@kcl.ac.uk.
  • Nademi Z; Immunology Department, Great Ormond Street Hospital, London, United Kingdom.
  • Deheragoda M; Institute of Liver Studies, MowatLabs, King's College Hospital, London, United Kingdom.
  • Zen Y; Institute of Liver Studies, MowatLabs, King's College Hospital, London, United Kingdom.
  • Elfeky R; Immunology Department, Great Ormond Street Hospital, London, United Kingdom; Bone Marrow Transplant Unit, Great Ormond Street Hospital, London, United Kingdom.
  • Worth A; Immunology Department, Great Ormond Street Hospital, London, United Kingdom.
  • Veys P; Bone Marrow Transplant Unit, Great Ormond Street Hospital, London, United Kingdom.
  • Mieli-Vergani G; Pediatric Liver Center for Hepatology, Gastroenterology, and Nutrition, King's College Hospital, London, United Kingdom; Institute of Liver Studies, MowatLabs, King's College Hospital, London, United Kingdom.
  • Davies EG; Immunology Department, Great Ormond Street Hospital, London, United Kingdom.
J Pediatr ; 209: 97-106.e2, 2019 06.
Article em En | MEDLINE | ID: mdl-30850087

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Colangite Esclerosante / Causas de Morte / Transplante de Células-Tronco Hematopoéticas / Doenças da Imunodeficiência Primária Tipo de estudo: Diagnostic_studies / Etiology_studies / Incidence_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limite: Child, preschool / Female / Humans / Infant / Male País/Região como assunto: Europa Idioma: En Revista: J Pediatr Ano de publicação: 2019 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Colangite Esclerosante / Causas de Morte / Transplante de Células-Tronco Hematopoéticas / Doenças da Imunodeficiência Primária Tipo de estudo: Diagnostic_studies / Etiology_studies / Incidence_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limite: Child, preschool / Female / Humans / Infant / Male País/Região como assunto: Europa Idioma: En Revista: J Pediatr Ano de publicação: 2019 Tipo de documento: Article